
Acardiac twinning is a rare congenital anomaly of monozygotic twin pregnancy characterized by formation of a malformed fetus with an absent or rudimentary (but nonfunctional) heart. Acardiac twinning, often results from abnormal placental vascular anastomoses. This leads to twin reversal arterial perfusion with complex pathophysiology. We report a case of acardiac-acephalus twins and briefly review the literature.