Noncompaction of the ventricular myocardium is a recognized primary genetic cardiomyopathy characterized by a distinctive (“spongy”) morphological appearance of the left ventricle1. It is a rare idiopathic cardiomyopathy with an incidence of about 0.05% 2,3. It is classified by the American Heart Association as a primary genetic cardiomyopathy 1 and is characterized by an altered myocardial wall with prominent trabeculae and deep intertrabecular recesses. The diagnosis of ventricular noncompaction is usually made using echocardiography and cardiac magnetic resonance imaging (MRI)1,2. We report a case of isolated biventricular noncompaction with complaints of dyspnoea.