Congenital gingival granular cell tumors (CGGCT) are rare lesions which have occasionally been reported in India. It is an uncommon benign soft tissue lesion that usually arises from alveolar mucosa of neonates and causes respiratory and feeding problems. Due to its clinical features and treatment approaches these cases have aroused interest of different disciplines. We reported a case of a 4 day old female child who presented with a mass attached to upper alveolar ridge which was protruding outside and obstructing the entire oral cavity leading to difficulty in feeding. The USG and histological findings of the mass makes it mandatory that CGGCT should be differentiated from the teratoma, hemangioma and lymphangioma.