ABSTRACT Background Desmoid tumors are slow growing deep fibromatoses with aggressive infiltration of adjacent tissue but without any metastatic potential(1,2,3). Case Presentation We report a female patient with desmoid tumor of the abdominal wall over appendicectomy scar who underwent primary resection. Preoperative evaluation included abdominal ultrasound, and computed tomography. The histology of this cases revealed a desmoid tumor. Conclusion Complete surgical resection is the first line management of this tumor entity.